Online ISSN: 2149-3189
2015
Monthly
Nicaea Medical Publishing
Türkiye

Class I pentalogy of Cantrell: a rare case report

Bayram Ali Dorum, Hilal Ozkan, Nilgun Koksal, Yasemin Denkboy Ongen
  • Bayram Ali Dorum (Author) Uludag University, School of Medicine, Division of Neonatology, Department of Pediatrics, Bursa
  • Hilal Ozkan (Author) Uludag University, School of Medicine, Division of Neonatology, Department of Pediatrics, Bursa
  • Nilgun Koksal (Author) Uludag University, School of Medicine, Division of Neonatology, Department of Pediatrics, Bursa
  • Yasemin Denkboy Ongen (Author) Department of Pediatrics, Uludag University School of Medicine, Bursa
DOI
https://doi.org/10.18621/eurj.293251
Abstract
Pentalogy of Cantrell is characterized by the presence of five major congenital defects involving the abdominal wall, pericardium, diaphragm, lower sternum and various cardiac abnormalities. This rare syndrome was described by Cantrell in 1958 and it has poor prognosis. We report here a case of class I Cantrell syndrome and our aim is to share difficulties experienced and review the related literature.
Keywords
Cantrell syndrome, ectopia cordis, omphalocele, ventricular diverticulum
References

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There are 11 references in total.
How to Cite
1.
Dorum BA, Ozkan H, Koksal N, Denkboy Ongen Y. Class I pentalogy of Cantrell: a rare case report. Eur Res J. 2017;3(1):83-86. doi:10.18621/eurj.293251
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Vol. 3 No. 1 (2017)

Article Information

  • Article Type Case Report
  • Submitted February 21, 2026
  • Published March 3, 2017
  • Issue Vol. 3 No. 1 (2017)
  • Section Case Report
  • File Downloads 1344
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